{"id":860,"date":"2022-10-08T08:12:36","date_gmt":"2022-10-08T08:12:36","guid":{"rendered":"https:\/\/medinaz.com\/blog\/?p=860"},"modified":"2022-10-08T08:12:37","modified_gmt":"2022-10-08T08:12:37","slug":"marfan-syndrome-mnemonic-for-usmle-neet-pg-fmge","status":"publish","type":"post","link":"https:\/\/medinaz.com\/blog\/2022\/10\/08\/marfan-syndrome-mnemonic-for-usmle-neet-pg-fmge\/","title":{"rendered":"Marfan syndrome Mnemonic: For USMLE, NEET PG, FMGE"},"content":{"rendered":"\n<p>What Marfan syndrome is and easy way to remember important marfan syndrome features with this Marfan syndrome Mnemonic \u201c<strong><span class=\"has-inline-color has-vivid-red-color\">MARFANS<\/span><\/strong>\u201d<\/p>\n\n\n\n<p>Marfan syndrome is an <a href=\"https:\/\/www.mayoclinic.org\/diseases-conditions\/marfan-syndrome\/symptoms-causes\/syc-20350782\" target=\"_blank\" rel=\"noreferrer noopener\">inherited disorder<\/a> of connective tissue (connective tissue supports and anchors our organs and other structures in our body). Marfan syndrome most commonly affects the eyes, heart, blood vessels and skeletal system.<\/p>\n\n\n\n<p>Important marfan syndrome features:<\/p>\n\n\n\n<ul><li>Autosomal dominant (with variable expression)<\/li><li>FBN1 gene mutation on chromosome 15, defective fibrillin-1&nbsp;<\/li><li>Tall with long extremities<\/li><li>Chest wall deformity (pectus carinatum [pigeon chest] or pectus excavatum<\/li><li>Hypermobile joints; long, tapering fingers and toes (arachnodactyly)<\/li><li>Cystic medial necrosis of aorta; aortic root aneurysm rupture or dissection (most common cause of death); mitral valve prolapse&nbsp;<\/li><li>Subluxated lense, retinal detachment<\/li><li>Negative Nitroprusside test (+ve in Homocystinuria)<\/li><\/ul>\n\n\n\n<p>Remember all the features with this Marfan syndrome Mnemonic: \u201c<strong><span class=\"has-inline-color has-vivid-red-color\">MARFANS<\/span><\/strong>\u201d<\/p>\n\n\n\n<p><strong><span class=\"has-inline-color has-vivid-red-color\">M<\/span><\/strong>itral valve prolapse (Medial necrosis of Aorta)<\/p>\n\n\n\n<p><strong><span class=\"has-inline-color has-vivid-red-color\">A<\/span><\/strong>ortic aneurysm<\/p>\n\n\n\n<p><strong><span class=\"has-inline-color has-vivid-red-color\">R<\/span><\/strong>etinal detachment<\/p>\n\n\n\n<p><strong><span class=\"has-inline-color has-vivid-red-color\">F<\/span><\/strong>ibrillin defect (<strong><span class=\"has-inline-color has-vivid-red-color\">F<\/span><\/strong>BN1 gene mutation on Ch. <strong><span class=\"has-inline-color has-vivid-red-color\">F<\/span><\/strong>ifteen)<\/p>\n\n\n\n<p><strong><span class=\"has-inline-color has-vivid-red-color\">A<\/span><\/strong>rachnodactyly<\/p>\n\n\n\n<p><strong><span class=\"has-inline-color has-vivid-red-color\">N<\/span><\/strong>egative <span class=\"has-inline-color has-vivid-red-color\"><strong>N<\/strong><\/span>itroprusside test (+ve in Homocystinuria)<\/p>\n\n\n\n<p><strong><span class=\"has-inline-color has-vivid-red-color\">S<\/span><\/strong>ubluxated lense<\/p>\n\n\n\n<figure class=\"wp-block-image size-full is-style-default\"><img loading=\"lazy\" width=\"500\" height=\"625\" src=\"https:\/\/medinaz.com\/blog\/wp-content\/uploads\/2022\/10\/Marfan-syndrome-mnemonic.jpeg\" alt=\"\" class=\"wp-image-861\" srcset=\"https:\/\/medinaz.com\/blog\/wp-content\/uploads\/2022\/10\/Marfan-syndrome-mnemonic.jpeg 500w, https:\/\/medinaz.com\/blog\/wp-content\/uploads\/2022\/10\/Marfan-syndrome-mnemonic-240x300.jpeg 240w\" sizes=\"(max-width: 500px) 100vw, 500px\" \/><\/figure>\n\n\n\n<p>You can also remember this way:<\/p>\n\n\n\n<p><strong>M<\/strong>:&nbsp;mitral valve prolapse<\/p>\n\n\n\n<p><strong>A<\/strong>:&nbsp;aortic dissection \/ aortic aneurysm<\/p>\n\n\n\n<p><strong>R<\/strong>:&nbsp;regurgitant aortic valve \/ retinal detachment<\/p>\n\n\n\n<p><strong>F<\/strong>:&nbsp;fibrillin-1 mutation<\/p>\n\n\n\n<p><strong>A<\/strong>:&nbsp;arm span &gt; height \/ arachnodactyly<\/p>\n\n\n\n<p><strong>N<\/strong>:&nbsp;near-sightness \/ nasal voice (high-arched palate)<\/p>\n\n\n\n<p><strong>S<\/strong>:&nbsp;scoliosis \/ subluxated lens<\/p>\n\n\n\n<p>Visit the Bookshop section of our website&nbsp;<a href=\"https:\/\/medinaz.com\/\" target=\"_blank\" rel=\"noreferrer noopener\">www.medinaz.com<\/a>&nbsp;&amp; install Medinaz App for Medinaz visual mnemonic &amp; High-yield books.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>What Marfan syndrome is and easy way to remember important marfan syndrome features with this Marfan syndrome Mnemonic \u201cMARFANS\u201d Marfan syndrome is an inherited disorder of connective tissue (connective tissue supports and anchors our organs and other structures in our body). Marfan syndrome most commonly affects the eyes, heart, blood vessels and skeletal system. Important<\/p>\n","protected":false},"author":1,"featured_media":864,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"ub_ctt_via":""},"categories":[96,43],"tags":[177,97],"featured_image_src":"https:\/\/medinaz.com\/blog\/wp-content\/uploads\/2022\/10\/Marfan-syndrome-mnemonic-1.001.jpeg","author_info":{"display_name":"Medinaz Academy","author_link":"https:\/\/medinaz.com\/blog\/author\/medinaz-blog-admin\/"},"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v19.4 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Marfan syndrome Mnemonic: For USMLE, NEET PG, FMGE -<\/title>\n<meta name=\"description\" content=\"Marfan syndrome Mnemonic: &quot;MARFANS&quot;. 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