{"id":951,"date":"2022-12-19T16:57:16","date_gmt":"2022-12-19T16:57:16","guid":{"rendered":"https:\/\/medinaz.com\/blog\/?p=951"},"modified":"2022-12-19T16:57:18","modified_gmt":"2022-12-19T16:57:18","slug":"medulloblastoma-brain-tumor-highyield-notes-for-usmle","status":"publish","type":"post","link":"https:\/\/medinaz.com\/blog\/2022\/12\/19\/medulloblastoma-brain-tumor-highyield-notes-for-usmle\/","title":{"rendered":"Medulloblastoma Brain Tumor Highyield Notes for USMLE"},"content":{"rendered":"\n<p>Medulloblastoma Brain Tumor Highyield Notes for USMLE, NEET PG, FMGE and Board Exams<\/p>\n\n\n\n<p>Medulloblastomas are the <strong>most common malignant brain tumor<\/strong> of <strong>childhood<\/strong><\/p>\n\n\n\n<p>It is accounting for ~20% of all primary CNS tumors among children.&nbsp;<\/p>\n\n\n\n<p>They arise from <strong>granule cell progenitors<\/strong> or from <strong>multipotent progenitors<\/strong> from the <strong>ventricular zone<\/strong>.\u00a0<\/p>\n\n\n\n<p>Approximately <strong>5%<\/strong> of children with medulloblastoma have an <strong>inherited syndrome<\/strong>, such as:<\/p>\n\n\n\n<ul><li><strong>Gorlin<\/strong><\/li><li><strong>Turcot<\/strong><\/li><li><strong>Li-Fraumeni<\/strong><\/li><\/ul>\n\n\n\n<h2>Histology of Medulloblastoma Brain Tumor:<\/h2>\n\n\n\n<p>Highly cellular tumors with abundant dark staining, round nuclei, and rosette formation (<strong>Homer-Wright rosettes<\/strong>).\u00a0<\/p>\n\n\n\n<h2>Medulloblastoma classification:<\/h2>\n\n\n\n<p>In the 2016 WHO pathologic classification, they have been divided into four molecular subgroups:<\/p>\n\n\n\n<p class=\"has-black-color has-text-color has-background\" style=\"background-color:#dfffe6\">1. WNT-activated (primarily affects children and has the best outcome);&nbsp;<\/p>\n\n\n\n<p class=\"has-black-color has-text-color has-background\" style=\"background-color:#dfffe6\">2. SHH-activated (affects adults, infants, and children with the younger patients having the better outcome and adults doing poorly);&nbsp;<\/p>\n\n\n\n<p class=\"has-black-color has-text-color has-background\" style=\"background-color:#dfffe6\">3. non-WNT\/non-SHH, group 3 (frequently has disseminated CNS disease at diagnosis and has the worst outcome); and&nbsp;<\/p>\n\n\n\n<p class=\"has-black-color has-text-color has-background\" style=\"background-color:#dfffe6\">4. non-WNT\/non-SHH, group 4 (30% have metastases at diagnosis, but 5-year progression-free survival is 95%).&nbsp;<\/p>\n\n\n\n<h2>Common presentation of Medulloblastoma:<\/h2>\n\n\n\n<p>Headache, dizziness, visual disturbances<\/p>\n\n\n\n<p>Truncal ataxia, seizures, sensory deficit<\/p>\n\n\n\n<p>Nausea, vomiting<\/p>\n\n\n\n<div class=\"wp-block-image is-style-default\"><figure class=\"aligncenter size-full\"><img loading=\"lazy\" width=\"600\" height=\"600\" src=\"https:\/\/medinaz.com\/blog\/wp-content\/uploads\/2022\/12\/Medulloblastoma-Brain-Tumor.jpeg\" alt=\"Medulloblastoma Brain Tumor\" class=\"wp-image-953\" srcset=\"https:\/\/medinaz.com\/blog\/wp-content\/uploads\/2022\/12\/Medulloblastoma-Brain-Tumor.jpeg 600w, https:\/\/medinaz.com\/blog\/wp-content\/uploads\/2022\/12\/Medulloblastoma-Brain-Tumor-300x300.jpeg 300w, https:\/\/medinaz.com\/blog\/wp-content\/uploads\/2022\/12\/Medulloblastoma-Brain-Tumor-150x150.jpeg 150w, https:\/\/medinaz.com\/blog\/wp-content\/uploads\/2022\/12\/Medulloblastoma-Brain-Tumor-370x370.jpeg 370w, https:\/\/medinaz.com\/blog\/wp-content\/uploads\/2022\/12\/Medulloblastoma-Brain-Tumor-45x45.jpeg 45w\" sizes=\"(max-width: 600px) 100vw, 600px\" \/><figcaption><strong><span class=\"has-inline-color has-black-color\">Medulloblastoma Brain Tumor<\/span><\/strong><\/figcaption><\/figure><\/div>\n\n\n\n<h2>Diagnosis of Medulloblastoma:<\/h2>\n\n\n\n<p><strong>MRI<\/strong> is the imaging modality of choice (<a href=\"https:\/\/www.cancer.gov\/rare-brain-spine-tumor\/tumors\/medulloblastoma\" target=\"_blank\" rel=\"noreferrer noopener\">ref<\/a>)<\/p>\n\n\n\n<p>Enhancing <strong>4th ventricular mass<\/strong><\/p>\n\n\n\n<p><strong>Hommer Wright rosettes<\/strong><\/p>\n\n\n\n<p>Sometimes associated with <strong>hydrocephalus<\/strong><\/p>\n\n\n\n<h2>Treatment of Medulloblastoma:<\/h2>\n\n\n\n<p>Maximal surgical resection, craniospinal irradiation, and chemotherapy with agents such as cisplatin, lomustine, cyclophosphamide, and vincristine.&nbsp;<\/p>\n\n\n\n<h2>Prognosis for Medulloblastoma:<\/h2>\n\n\n\n<p>65-85% Survival dependent on stage\/type<\/p>\n\n\n\n<p>Poorer prognosis in infants<\/p>\n\n\n\n<p><strong>Reference<\/strong>: Harrison&#8217;s Principles of Internal Medicine, 20th Edition<\/p>\n\n\n\n<p><strong>Check other Medinaz Highyield Visual Notes:<\/strong><\/p>\n\n\n\n<p class=\"has-vivid-cyan-blue-color has-text-color\"><a href=\"https:\/\/medinaz.com\/blog\/2021\/09\/28\/bacterial-causes-of-diarrhea-illustrated-medicine-notes\/\" target=\"_blank\" rel=\"noreferrer noopener\">Bacterial causes of diarrhoea &#8211; Illustrated highyield notes<\/a><\/p>\n\n\n\n<p class=\"has-vivid-cyan-blue-color has-text-color\"><a href=\"https:\/\/medinaz.com\/blog\/2021\/07\/25\/osteogenesis-imperfecta\/\" target=\"_blank\" rel=\"noreferrer noopener\">Osteogenesis Imperfecta &#8211; Illustrated highyield notes<\/a><\/p>\n\n\n\n<p class=\"has-vivid-cyan-blue-color has-text-color\"><a href=\"https:\/\/medinaz.com\/blog\/category\/medical-notes\/medical-mnemonics\/\" target=\"_blank\" rel=\"noreferrer noopener\">Medinaz Visual mnemonics<\/a><\/p>\n","protected":false},"excerpt":{"rendered":"<p>Medulloblastoma Brain Tumor Highyield Notes for USMLE, NEET PG, FMGE and Board Exams Medulloblastomas are the most common malignant brain tumor of childhood It is accounting for ~20% of all primary CNS tumors among children.&nbsp; They arise from granule cell progenitors or from multipotent progenitors from the ventricular zone.\u00a0 Approximately 5% of children with medulloblastoma<\/p>\n","protected":false},"author":1,"featured_media":956,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"ub_ctt_via":""},"categories":[43,44],"tags":[83,189],"featured_image_src":"https:\/\/medinaz.com\/blog\/wp-content\/uploads\/2022\/12\/Medulloblastoma-Brain-Tumor-1.jpeg","author_info":{"display_name":"Medinaz Academy","author_link":"https:\/\/medinaz.com\/blog\/author\/medinaz-blog-admin\/"},"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v19.4 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Medulloblastoma Brain Tumor Highyield Notes for USMLE<\/title>\n<meta name=\"description\" content=\"Medulloblastoma Brain Tumor Highyield visual Notes for USMLE, NEET PG, FMGE and Board Exams. 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